Nükhet ALADAĞ ÇİFTDEMİR1, Selman GÖKALP2, Tuba EREN1

1Department of Pediatrics, Trakya University Faculty of Medicine, Edirne, Turkey
2Department of Pediatrics, Cerrahpaşa University Faculty of Medicine, Istanbul, Turkey

Keywords: Behçet’s disease, intracardiac thrombosis, pulmonary artery aneurysm

Abstract

Behçet’s disease (BD) is a rare, multisystemic, chronic vasculitic disorder with unknown etiology. Intracardiac thrombus formation and pulmonary artery aneurysm in BD are very rare. The treatment protocol in patients with vascular involvement, particularly those with pulmonary artery aneurysm accompanied by thrombosis, have not been clearly defined. In this article, we report an exceptional case, who had been treated unsuccessfully with a combination of anti-inflammatory/immunosuppressive therapy and thrombolytic agents, to discuss the poor prognosis of pulmonary artery aneurysm accompanying intracardiac thrombosis in juvenile BD.